Imaging findings in Steideles complex

Description

Steidele's complex is an eponym to interrupted aortic arch (IAA), which is characterised by complete anatomic discontinuity between the aortic arch and the descending aorta (DA). It is a very rare congenital anomaly that occurs in 19 per million live births.1 Based on the site of interruption, it is classified into three types: type A (30%–40%) when it occurs beyond the left subclavian artery, type B (51%–70%) when it occurs between the left carotid artery and the left subclavian artery and type C (1%–5%) when it occurs between the brachiocephalic artery and the left common carotid artery.2 DA originates from the pulmonary artery through a patent ductus arteriosus (PDA). IAA is invariably associated with a ventricular septal defect (VSD) in majority of cases. IAA is associated with a high mortality rate of 75% at 1 month and 90% at 1 year, in the absence of operative intervention.3 We describe a...

from Cases via ola Kala on Inoreader http://ift.tt/2rwD3ac
via IFTTT

http://ift.tt/2sIbvST